A 74-year-old women with no medical history was admitted to the emergency room with sudden blindness of the left eye. The previous days she had suffered from a painful and swollen neck, jaw claudication and mild temporal headache. Two days before admission she felt a numbness on the left side of her tongue. Physical examination showed dysarthric speech and oedema of the skin and neck. There was a normal consensual response but no direct response with examination of the left pupillary reflex. Blood results revealed elevated ESR (114 mm/h), thrombocytes (750/nl), WBC (17.8 /nl) and CRP (300 mg/l). Ophthalmological examination showed a pale optic disc in the left eye, caused by a central retinal artery occlusion (CRAO). Two days later, the patient suffered from pain when moving her tongue during eating and speaking. We saw progression of the dysarthric speech and a left-sided deviation of the tongue with a blue discoloration, which progressed during the day (figure 1). After a couple of days there was a demarcated necrotic aspect on the left side of the tongue with a greyish discoloration (figure 2).